Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Sema4, |
RCV002255809 | SCV002529234 | uncertain significance | Hereditary cancer-predisposing syndrome | 2021-12-15 | criteria provided, single submitter | curation | |
Ambry Genetics | RCV002255809 | SCV005552978 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-07-23 | criteria provided, single submitter | clinical testing | The p.L263R variant (also known as c.788T>G), located in coding exon 6 of the BRIP1 gene, results from a T to G substitution at nucleotide position 788. The leucine at codon 263 is replaced by arginine, an amino acid with dissimilar properties. This amino acid position is conserved. In addition, this alteration is predicted to be deleterious by in silico analysis. Based on the available evidence, the clinical significance of this variant remains unclear. |