Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Quest Diagnostics Nichols Institute San Juan Capistrano | RCV000759000 | SCV000888004 | uncertain significance | not provided | 2018-02-07 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001855913 | SCV002131523 | uncertain significance | Familial cancer of breast; Fanconi anemia complementation group J | 2021-06-26 | criteria provided, single submitter | clinical testing | This sequence change replaces asparagine with serine at codon 306 of the BRIP1 protein (p.Asn306Ser). The asparagine residue is weakly conserved and there is a small physicochemical difference between asparagine and serine. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be tolerated, but these predictions have not been confirmed by published functional studies and their clinical significance is uncertain. This variant has not been reported in the literature in individuals with BRIP1-related conditions. ClinVar contains an entry for this variant (Variation ID: 619664). This variant is not present in population databases (ExAC no frequency). |