Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetics Laboratory, |
RCV001420198 | SCV001622618 | likely pathogenic | See cases | 2021-04-26 | criteria provided, single submitter | clinical testing | PM2_supporting;PM6_moderate;PP2_supporting;PP3_supporting |
Gene |
RCV004720906 | SCV005326772 | pathogenic | not provided | 2023-08-26 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis suggests that this missense variant does not alter protein structure/function, but splice predictors indicate that the variant may lead to abnormal gene splicing; This variant is associated with the following publications: (PMID: 32376980) |