Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Broad Center for Mendelian Genomics, |
RCV001258275 | SCV001435200 | benign | Central core myopathy | criteria provided, single submitter | research | The p.Glu646Asp variant in ATP13A4 has been identified in 6 individuals with autism spectrum disorder (PMID: 15925480). However, this variant is classified as benign for autism spectrum disorder because it has been identified in >5% of European (non-Finnish) chromosomes by ExAC (http://gnomad.broadinstitute.org/). | |
Breakthrough Genomics, |
RCV004716715 | SCV005298372 | benign | not provided | criteria provided, single submitter | not provided | ||
Prevention |
RCV003918810 | SCV004732013 | benign | ATP13A4-related disorder | 2020-09-04 | no assertion criteria provided | clinical testing | This variant is classified as benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |