Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001985785 | SCV002261221 | uncertain significance | Severe combined immunodeficiency due to CARD11 deficiency; BENTA disease | 2023-01-10 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may create or strengthen a splice site. ClinVar contains an entry for this variant (Variation ID: 1479784). This variant has been observed in individual(s) with clinical features of CARD11-related conditions (Invitae). It has also been observed to segregate with disease in related individuals. This variant is present in population databases (no rsID available, gnomAD 0.006%). This sequence change falls in intron 8 of the CARD11 gene. It does not directly change the encoded amino acid sequence of the CARD11 protein. |