Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001762722 | SCV001990092 | likely pathogenic | not provided | 2024-07-22 | criteria provided, single submitter | clinical testing | Identified as a heterozygous variant in patients with clinical features of a CARD11-related disorder referred for genetic testing at GeneDx and in published literature (PMID: 38231347); Not observed at significant frequency in large population cohorts (gnomAD); Published functional studies suggest decreased protein function, although further experiments are needed to determine this conclusively (PMID: 33202260); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 37037469, 38231347, 33202260) |
Ce |
RCV001762722 | SCV004042287 | likely pathogenic | not provided | 2024-03-01 | criteria provided, single submitter | clinical testing | CARD11: PM2, PM5, PP2, PS3:Supporting, PS4:Supporting |
University of Washington Center for Mendelian Genomics, |
RCV001543387 | SCV001761945 | likely pathogenic | Immunodeficiency 11b with atopic dermatitis | no assertion criteria provided | research |