Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genome- |
RCV001554684 | SCV001775967 | benign | BENTA disease | 2021-07-14 | criteria provided, single submitter | clinical testing | |
Genome- |
RCV001554685 | SCV001775968 | benign | Severe combined immunodeficiency due to CARD11 deficiency | 2021-07-14 | criteria provided, single submitter | clinical testing | |
Genome- |
RCV001554686 | SCV001775969 | benign | Immunodeficiency 11b with atopic dermatitis | 2021-07-14 | criteria provided, single submitter | clinical testing | |
Unidad de Genómica Garrahan, |
RCV003399362 | SCV004102305 | benign | not specified | 2023-11-12 | criteria provided, single submitter | clinical testing | This variant is classified as Benign based on local population frequency. This variant was detected in 38% of patients studied by a panel of primary immunodeficiencies. Number of patients: 36. Only high quality variants are reported. |