Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV004771679 | SCV005382352 | uncertain significance | BENTA disease | 2023-05-20 | criteria provided, single submitter | clinical testing | The observed missense variant c.3232G>C(p.Val1078Leu) in CARD11 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The c.3232G>C variant has 0.001% allele frequency in gnomAD Exomes. The amino acid Valine at position 1078 is changed to a Leucine changing protein sequence and it might alter its composition and physicochemical properties. The reference amino acid p.Val1078Leu in CARD11 is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. Computational evidence (Polyphen-Benign, SIFT-Tolerated and Mutation Taster-Disease causing) predicts conflicting evidence on protein structure and function for this variant. For these reasons, this variant has been classified as Uncertain Significance. |