Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV004818816 | SCV005438678 | uncertain significance | Intellectual disability, autosomal dominant 40 | 2023-06-22 | criteria provided, single submitter | clinical testing | The observed missense variant c.785C>Tp.Ala262Val in CHAMP1 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.Ala262Val variant is absent in gnomAD Exomes. The amino acid Ala at position 262 is changed to a Val changing protein sequence and it might alter its composition and physico-chemical properties. Multiple lines of computational evidence Polyphen-Benign, SIFT-Tolerated and Mutation Taster-polymorphic predict no damaging effect on protein structure and function for this variant. The reference amino acid p.Ala262Val in CHAMP1 is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Uncertain Significance. |