Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Counsyl | RCV000670131 | SCV000794948 | pathogenic | GNPTG-mucolipidosis | 2017-10-23 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001868240 | SCV002230641 | pathogenic | not provided | 2021-07-28 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This variant has been observed in individual(s) with mucolipidosis III gamma (PMID: 27896079, 26935170). ClinVar contains an entry for this variant (Variation ID: 554488). This variant is not present in population databases (ExAC no frequency). This sequence change creates a premature translational stop signal (p.Glu110*) in the GNPTG gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in GNPTG are known to be pathogenic (PMID: 19370764, 20301784). |