Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Mayo Clinic Laboratories, |
RCV001508925 | SCV001715363 | uncertain significance | not provided | 2019-04-15 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001508925 | SCV002111548 | uncertain significance | not provided | 2022-08-23 | criteria provided, single submitter | clinical testing | This sequence change replaces cysteine with tyrosine at codon 1589 of the MYO18B protein (p.Cys1589Tyr). The cysteine residue is weakly conserved and there is a large physicochemical difference between cysteine and tyrosine. This variant is present in population databases (rs375717740, gnomAD 0.07%), including at least one homozygous and/or hemizygous individual. This variant has not been reported in the literature in individuals affected with MYO18B-related conditions. ClinVar contains an entry for this variant (Variation ID: 1163670). Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Not Available"; PolyPhen-2: "Benign"; Align-GVGD: "Not Available"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Ambry Genetics | RCV002564265 | SCV003650042 | uncertain significance | Inborn genetic diseases | 2024-12-02 | criteria provided, single submitter | clinical testing | The c.4766G>A (p.C1589Y) alteration is located in exon 29 (coding exon 28) of the MYO18B gene. This alteration results from a G to A substitution at nucleotide position 4766, causing the cysteine (C) at amino acid position 1589 to be replaced by a tyrosine (Y). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Revvity Omics, |
RCV003130532 | SCV003817810 | uncertain significance | Klippel-Feil anomaly-myopathy-facial dysmorphism syndrome | 2021-11-11 | criteria provided, single submitter | clinical testing |