Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Prevention |
RCV004729689 | SCV005339923 | likely pathogenic | GATA2-related disorder | 2024-06-12 | no assertion criteria provided | clinical testing | The GATA2 c.1018-26_1033delinsAGC variant is predicted to result in a frameshift and premature protein termination (p.Ala341Profs*42). To our knowledge, this variant has not been reported in the literature or in a large population database, indicating this variant is rare. Frameshift variants in GATA2 are expected to be pathogenic. This variant is interpreted as likely pathogenic. |