Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001368018 | SCV001564393 | uncertain significance | Deafness-lymphedema-leukemia syndrome; Monocytopenia with susceptibility to infections | 2024-01-22 | criteria provided, single submitter | clinical testing | This sequence change replaces lysine, which is basic and polar, with asparagine, which is neutral and polar, at codon 405 of the GATA2 protein (p.Lys405Asn). This variant is present in population databases (rs779797858, gnomAD 0.003%). This missense change has been observed in individual(s) with lymphedema (PMID: 29906362). ClinVar contains an entry for this variant (Variation ID: 1058839). Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is expected to disrupt GATA2 protein function with a positive predictive value of 95%. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Baylor Genetics | RCV003469607 | SCV004198635 | uncertain significance | Acute myeloid leukemia | 2023-08-05 | criteria provided, single submitter | clinical testing |