Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Prevention |
RCV000984842 | SCV001132731 | pathogenic | not provided | 2017-05-23 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001386684 | SCV001587018 | pathogenic | Deafness-lymphedema-leukemia syndrome; Monocytopenia with susceptibility to infections | 2020-08-02 | criteria provided, single submitter | clinical testing | Loss-of-function variants in GATA2 are known to be pathogenic (PMID: 21670465, 23223431). This variant has been observed in individual(s) with GATA2 deficiency (PMID: 21765025, 26702063). This variant is also known as c.599_600insG in the literature. ClinVar contains an entry for this variant (Variation ID: 29715). The frequency data for this variant in the population databases is considered unreliable, as metrics indicate poor data quality at this position in the ExAC database. This sequence change creates a premature translational stop signal (p.Ser201*) in the GATA2 gene. It is expected to result in an absent or disrupted protein product. For these reasons, this variant has been classified as Pathogenic. |
Molecular Pathology Research Laboratory, |
RCV001542189 | SCV001760857 | pathogenic | Deafness-lymphedema-leukemia syndrome; GATA2 deficiency with susceptibility to MDS/AML | 2021-07-06 | criteria provided, single submitter | curation | PVS1, PS4, PM2 |
Genetic Services Laboratory, |
RCV000984842 | SCV002069674 | pathogenic | not provided | 2021-02-23 | criteria provided, single submitter | clinical testing | |
OMIM | RCV000022567 | SCV000043856 | pathogenic | Monocytopenia with susceptibility to infections | 2011-09-08 | no assertion criteria provided | literature only |