Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV001815069 | SCV002061923 | uncertain significance | not specified | 2019-07-30 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV002478044 | SCV002786640 | uncertain significance | Optic atrophy 10 with or without ataxia, intellectual disability, and seizures | 2022-03-03 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV003772270 | SCV004672952 | uncertain significance | not provided | 2022-06-27 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Not Available"; PolyPhen-2: "Possibly Damaging"; Align-GVGD: "Not Available"). ClinVar contains an entry for this variant (Variation ID: 850490). This variant has not been reported in the literature in individuals affected with RTN4IP1-related conditions. Information on the frequency of this variant in the gnomAD database is not available, as this variant may be reported differently in the database. This variant, c.104_117delinsGAAGGATT, is a complex sequence change that results in the deletion of 5 and insertion of 3 amino acid(s) in the RTN4IP1 protein (p.Thr35_Arg39delinsArgArgIle). |