Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000822084 | SCV000962870 | uncertain significance | Early myoclonic encephalopathy | 2022-07-25 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be tolerated. This sequence change replaces histidine, which is basic and polar, with tyrosine, which is neutral and polar, at codon 614 of the JMJD1C protein (p.His614Tyr). This variant is present in population databases (rs779543715, gnomAD 0.005%). This variant has not been reported in the literature in individuals affected with JMJD1C-related conditions. ClinVar contains an entry for this variant (Variation ID: 664071). |
Ambry Genetics | RCV004629354 | SCV005127355 | uncertain significance | not specified | 2024-03-26 | criteria provided, single submitter | clinical testing | The c.1840C>T (p.H614Y) alteration is located in exon 8 (coding exon 8) of the JMJD1C gene. This alteration results from a C to T substitution at nucleotide position 1840, causing the histidine (H) at amino acid position 614 to be replaced by a tyrosine (Y). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |