Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004605749 | SCV005099051 | uncertain significance | Inborn genetic diseases | 2024-03-18 | criteria provided, single submitter | clinical testing | The c.436A>G (p.I146V) alteration is located in exon 7 (coding exon 7) of the BBS4 gene. This alteration results from a A to G substitution at nucleotide position 436, causing the isoleucine (I) at amino acid position 146 to be replaced by a valine (V). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Fulgent Genetics, |
RCV005003774 | SCV005630874 | uncertain significance | Bardet-Biedl syndrome 4 | 2024-02-13 | criteria provided, single submitter | clinical testing |