Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Counsyl | RCV000668779 | SCV000793432 | uncertain significance | Usher syndrome type 1F | 2017-08-16 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001868225 | SCV002189272 | likely benign | not provided | 2024-04-22 | criteria provided, single submitter | clinical testing | |
Gene |
RCV001868225 | SCV003933433 | uncertain significance | not provided | 2024-10-29 | criteria provided, single submitter | clinical testing | Frameshift variant predicted to result in protein truncation, as the last 178 amino acids are replaced with 69 different amino acids, and other loss-of-function variants have been reported downstream in HGMD; Has not been previously published as pathogenic or benign to our knowledge |
Breakthrough Genomics, |
RCV001868225 | SCV005190756 | uncertain significance | not provided | criteria provided, single submitter | not provided | ||
Women's Health and Genetics/Laboratory Corporation of America, |
RCV004768530 | SCV005380734 | uncertain significance | not specified | 2024-08-09 | criteria provided, single submitter | clinical testing | Variant summary: PCDH15 c.5332dupT (p.Cys1778LeufsX70) results in a premature termination codon, predicted to cause a truncation of the encoded protein or absence of the protein. Truncating variants in the last exon of PCDH15 have uncertain impact on protein function. The variant allele was found at a frequency of 2.8e-05 in 181112 control chromosomes in the gnomAD database, including 1 homozygotes. The available data on variant occurrences in the general population are insufficient to allow any conclusion about variant significance. To our knowledge, no occurrence of c.5332dupT in individuals affected with Usher Syndrome Type 1F and no experimental evidence demonstrating its impact on protein function have been reported. ClinVar contains an entry for this variant (Variation ID: 553355). Based on the evidence outlined above, the variant was classified as uncertain significance. |