Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001212332 | SCV001383913 | uncertain significance | Long QT syndrome | 2022-03-08 | criteria provided, single submitter | clinical testing | This variant has not been reported in the literature in individuals affected with CAV3-related conditions. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be disruptive. ClinVar contains an entry for this variant (Variation ID: 942355). This variant is not present in population databases (gnomAD no frequency). This sequence change replaces threonine, which is neutral and polar, with isoleucine, which is neutral and non-polar, at codon 127 of the CAV3 protein (p.Thr127Ile). |
Revvity Omics, |
RCV003145390 | SCV003829262 | uncertain significance | not provided | 2021-05-17 | criteria provided, single submitter | clinical testing |