Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000485433 | SCV000573790 | pathogenic | not provided | 2017-02-24 | criteria provided, single submitter | clinical testing | The c.31_32insGGC pathogenic variant in the KRAS gene has not been reported previously as a pathogenic variant, nor as a benign variant, to our knowledge. The c.31_32insGGC variant causes an in-frame deletion of one amino acid, Alanine 11, and insertion at the same location of two amino acids, Glycine and Proline, denoted p.Ala11delinsGlyPro. This amino acid change occurs at a position in the GTP-binding region that is conserved across species. In silico analysis is inconsistent in its predictions as to whether or not the variant is damaging to the protein structure/function. The c.31_32insGGC variant is not observed in large population cohorts (Lek et al., 2016; 1000 Genomes Consortium et al., 2015; Exome Variant Server). We interpret c.31_32insGGC as a pathogenic variant. |