Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV002267433 | SCV002549524 | likely pathogenic | not provided | 2022-01-13 | criteria provided, single submitter | clinical testing | Canonical splice site variant predicted to result in in-frame deletion within a critical region. Variant damages or destroys the canonical splice donor site in intron 6, and is expected to cause abnormal gene splicing; if the splice outcome is exon skip, the loss of the encoded residues in the triple helical region is expected to disrupt normal protein folding and function; Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 35005319, 24337245) |
Fulgent Genetics, |
RCV005042766 | SCV005679753 | pathogenic | X-linked Alport syndrome | 2024-01-08 | criteria provided, single submitter | clinical testing |