Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002643888 | SCV003511606 | likely benign | not provided | 2024-07-05 | criteria provided, single submitter | clinical testing | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV004690374 | SCV005186103 | uncertain significance | not specified | 2024-05-01 | criteria provided, single submitter | clinical testing | Variant summary: COL4A5 c.730A>T (p.Ile244Phe) results in a non-conservative amino acid change in the encoded protein sequence. Three of five in-silico tools predict a benign effect of the variant on protein function. The variant allele was found at a frequency of 1.1e-05 in 183247 control chromosomes (gnomAD). The available data on variant occurrences in the general population are insufficient to allow any conclusion about variant significance. To our knowledge, no occurrence of c.730A>T in individuals affected with X-Linked Alport Syndrome and no experimental evidence demonstrating its impact on protein function have been reported. ClinVar contains an entry for this variant (Variation ID: 2193026). Based on the evidence outlined above, the variant was classified as uncertain significance. |