Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002271346 | SCV004295621 | pathogenic | Predisposition to invasive fungal disease due to CARD9 deficiency | 2023-06-27 | criteria provided, single submitter | clinical testing | This variant is present in population databases (rs753050033, gnomAD 0.05%). This sequence change creates a premature translational stop signal (p.Asp274Glyfs*61) in the CARD9 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in CARD9 are known to be pathogenic (PMID: 19864672, 24131138, 24231284). This premature translational stop signal has been observed in individual(s) with clinical features of CARD9 deficiency (PMID: 24231284). This variant is also known as c.819-820insG (p.D274fsX60). ClinVar contains an entry for this variant (Variation ID: 1698432). For these reasons, this variant has been classified as Pathogenic. |
Juno Genomics, |
RCV002271346 | SCV005416305 | likely pathogenic | Predisposition to invasive fungal disease due to CARD9 deficiency | criteria provided, single submitter | clinical testing | PM2_Supporting+PM3_Strong+PP4 | |
OMIM | RCV002271346 | SCV002555554 | risk factor | Predisposition to invasive fungal disease due to CARD9 deficiency | 2022-07-27 | no assertion criteria provided | literature only |