Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
3billion, |
RCV000074440 | SCV002521058 | pathogenic | Predisposition to invasive fungal disease due to CARD9 deficiency | 2022-05-22 | criteria provided, single submitter | clinical testing | The variant is observed at an extremely low frequency in the gnomAD v2.1.1 dataset (total allele frequency: <0.001%). Stop-gained (nonsense): predicted to result in a loss or disruption of normal protein function through nonsense-mediated decay (NMD) or protein truncation. Multiple pathogenic variants are reported downstream of the variant. The variant has been observed in multiple (>3) similarly affected unrelated individuals (PMID:24131138) and reported to co-segregate with the disease in at least one similarly affected individuals in the same family or similarly affected unrelated family (PMID:24131138). Therefore, this variant is classified as pathogenic according to the recommendation of ACMG/AMP guideline. |
Fulgent Genetics, |
RCV000074440 | SCV002806728 | pathogenic | Predisposition to invasive fungal disease due to CARD9 deficiency | 2021-10-17 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000074440 | SCV003441325 | pathogenic | Predisposition to invasive fungal disease due to CARD9 deficiency | 2024-07-19 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Gln289*) in the CARD9 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in CARD9 are known to be pathogenic (PMID: 19864672, 24131138, 24231284). This variant is present in population databases (rs398122363, gnomAD 0.006%). This premature translational stop signal has been observed in individual(s) with clinical features of CARD9-related conditions (PMID: 24131138, 25702837, 32888943). ClinVar contains an entry for this variant (Variation ID: 88852). For these reasons, this variant has been classified as Pathogenic. |
OMIM | RCV000074440 | SCV000108456 | risk factor | Predisposition to invasive fungal disease due to CARD9 deficiency | 2013-10-31 | no assertion criteria provided | literature only |