Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000934218 | SCV001079936 | likely benign | not provided | 2024-09-06 | criteria provided, single submitter | clinical testing | |
Al Jalila Children’s Genomics Center, |
RCV001731981 | SCV001984610 | likely benign | not specified | 2020-09-24 | criteria provided, single submitter | clinical testing | |
Revvity Omics, |
RCV000934218 | SCV004236781 | uncertain significance | not provided | 2023-10-26 | criteria provided, single submitter | clinical testing | |
Department of Pathology and Laboratory Medicine, |
RCV000934218 | SCV001552993 | uncertain significance | not provided | no assertion criteria provided | clinical testing | The NALCN p.Y832C variant was not identified in the literature but was identified in dbSNP (ID: rs549182297) and ClinVar (classified as likely benign by Invitae). The variant was identified in control databases in 176 of 282618 chromosomes (1 homozygous) at a frequency of 0.0006227, and was observed at the highest frequency in the South Asian population in 171 of 30614 chromosomes (1 homozygous) (freq: 0.005586) (Genome Aggregation Database March 6, 2019, v2.1.1). The p.Y832 residue is conserved in mammals and more distantly related organisms, and computational analyses (MUT Assesor, PolyPhen-2, SIFT, MutationTaster, Revel, FATHMM, MetaLR, DANN) suggest that the variant may impact the protein; however, this information is not predictive enough to assume pathogenicity. The variant occurs outside of the splicing consensus sequence and in silico or computational prediction software programs (Splice AI exome) do not predict a deleterious effect on splicing. In summary, based on the above information the clinical significance of this variant cannot be determined with certainty at this time. This variant is classified as a variant of uncertain significance. | |
Prevention |
RCV004533590 | SCV004750371 | likely benign | NALCN-related disorder | 2023-03-28 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |