Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000760947 | SCV000890843 | likely pathogenic | not provided | 2020-02-08 | criteria provided, single submitter | clinical testing | Nonsense variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss-of-function is a known mechanism of disease; Not observed in large population cohorts (Lek et al., 2016); Has not been previously published as pathogenic or benign to our knowledge |
Labcorp Genetics |
RCV002533855 | SCV003228968 | pathogenic | Generalized epilepsy with febrile seizures plus, type 9 | 2022-09-18 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Glu132*) in the STX1B gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in STX1B are known to be pathogenic (PMID: 25362483). For these reasons, this variant has been classified as Pathogenic. ClinVar contains an entry for this variant (Variation ID: 620559). This variant has not been reported in the literature in individuals affected with STX1B-related conditions. This variant is not present in population databases (gnomAD no frequency). |