Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002606434 | SCV003504422 | uncertain significance | Cranioectodermal dysplasia 1 | 2021-12-20 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be tolerated. This variant has not been reported in the literature in individuals affected with IFT122-related conditions. This variant is present in population databases (rs369704793, gnomAD 0.004%). This sequence change replaces glutamic acid, which is acidic and polar, with glycine, which is neutral and non-polar, at codon 1014 of the IFT122 protein (p.Glu1014Gly). |
Fulgent Genetics, |
RCV002606434 | SCV005661393 | uncertain significance | Cranioectodermal dysplasia 1 | 2024-06-09 | criteria provided, single submitter | clinical testing |