Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV000600547 | SCV000710885 | likely benign | not specified | 2017-01-19 | criteria provided, single submitter | clinical testing | p.Arg269Gln in exon 4 of BSND: This variant is not expected to have clinical sig nificance due to a lack of conservation across species, including mammals. Of no te, >10 mammals have a glutamine (Gln) at this position. In addition, computatio nal prediction tools do not suggest a high likelihood of impact to the protein. It has been identified in 10/66322 European chromosomes by the Exome Aggregation Consortium (ExAC, http://exac.broadinstitute.org; dbSNP rs199832638). |
Labcorp Genetics |
RCV002532710 | SCV003292074 | uncertain significance | not provided | 2022-05-23 | criteria provided, single submitter | clinical testing | This sequence change replaces arginine, which is basic and polar, with glutamine, which is neutral and polar, at codon 269 of the BSND protein (p.Arg269Gln). This variant is present in population databases (rs199832638, gnomAD 0.02%). This variant has not been reported in the literature in individuals affected with BSND-related conditions. ClinVar contains an entry for this variant (Variation ID: 504521). Algorithms developed to predict the effect of missense changes on protein structure and function output the following: SIFT: "Tolerated"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0". The glutamine amino acid residue is found in multiple mammalian species, which suggests that this missense change does not adversely affect protein function. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Gene |
RCV002532710 | SCV005081509 | uncertain significance | not provided | 2024-01-05 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant does not alter protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |
Breakthrough Genomics, |
RCV002532710 | SCV005257968 | likely benign | not provided | criteria provided, single submitter | not provided |