Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV000039821 | SCV000063512 | uncertain significance | not specified | 2015-08-11 | criteria provided, single submitter | clinical testing | Variant classified as Uncertain Significance - Favor Benign. The p.Gly284Asp var iant in BSND has not been reported in individuals with hearing loss or Bartter s yndrome, but it has been identified in 0.2% (22/10390) African chromosomes by th e Exome Aggregation Consortium (ExAC, http://exac.broadinstitute.org; dbSNP rs15 0426464). One in vitro functional study provides some evidence that the p.Gly284 Asp variant may have a mild impact on protein function; however, this assay may not accurately represent biological function (Sile 2007). Computational predicti on tools and conservation analyses suggest that the p.Gly284Asp variant may not impact the protein, though this information is not predictive enough to rule out pathogenicity. In summary, while the clinical significance of the p.Gly284Asp v ariant is uncertain, the frequency and computational data suggest that it is mor e likely to be benign. |
Eurofins Ntd Llc |
RCV000727291 | SCV000707297 | uncertain significance | not provided | 2017-04-04 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000727291 | SCV001058068 | likely benign | not provided | 2025-01-12 | criteria provided, single submitter | clinical testing | |
Gene |
RCV000727291 | SCV001874080 | uncertain significance | not provided | 2024-12-31 | criteria provided, single submitter | clinical testing | Has been previously reported in a study to determine if partial loss of function variants are protective to the development of hypertension; has not been published in association with BSND-related disorders (PMID: 17954364); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 17954364) |