Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000131735 | SCV000186776 | pathogenic | Hereditary cancer-predisposing syndrome | 2013-05-21 | criteria provided, single submitter | clinical testing | This alteration is expected to result in loss of function by premature protein truncation or nonsense-mediated mRNA decay. As such, this alteration is interpreted as a disease-causing mutation. |
Labcorp Genetics |
RCV001849944 | SCV002138151 | pathogenic | Fanconi anemia complementation group O | 2021-03-21 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This variant has been observed in individual(s) with a family history of ovarian cancer (PMID: 26261251). ClinVar contains an entry for this variant (Variation ID: 142544). This variant is not present in population databases (ExAC no frequency). This sequence change creates a premature translational stop signal (p.Ser53Leufs*6) in the RAD51C gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in RAD51C are known to be pathogenic (PMID: 20400964, 21990120, 24800917). |