Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001228895 | SCV001401321 | uncertain significance | Fanconi anemia complementation group O | 2022-07-12 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. ClinVar contains an entry for this variant (Variation ID: 956146). This variant has not been reported in the literature in individuals affected with RAD51C-related conditions. This variant is not present in population databases (gnomAD no frequency). This sequence change affects the initiator methionine of the RAD51C mRNA. The next in-frame methionine is located at codon 10. |
German Consortium for Hereditary Breast and Ovarian Cancer, |
RCV004690022 | SCV005184346 | uncertain significance | Hereditary breast ovarian cancer syndrome | 2024-05-03 | criteria provided, single submitter | curation | According to the ACMG SVI adaptation criteria we chose these criteria: PM2 (supporting pathogenic): absent from gnomAD, BS3 (strong benign): alternative start codon at M10 variants in the first methionine are homologous recombination proficient https://www.sciencedirect.com/science/article/pii/S156878642400020X?via%3Dihub |