Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
St. |
RCV003444455 | SCV004171520 | likely pathogenic | Breast-ovarian cancer, familial, susceptibility to, 3 | 2023-10-26 | criteria provided, single submitter | clinical testing | The RAD51C c.572-1854_705+2812del variant is a gross deletion of the genomic region encompassing exon 4 of the RAD51C gene. The 5’ end is likely confined to intron 3. The 3’ end of this event is likely confined to intron 4. This deletion is predicted to cause a frameshift and the creation of a premature stop codon (p.Glu191Glyfs*16). This change is predicted to cause protein truncation or absence of protein due to nonsense-mediated decay. Deletions including exon 4 of RAD51C have been reported in the literature in individuals with hereditary breast and ovarian cancer (PMID: 28888541, 32107557, 33219106, 34487234). Loss-of-function variants in RAD51C are known to be pathogenic (PMID: 20400964, 21990120). In summary, this variant meets criteria to be classified as likely pathogenic. |