Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000760391 | SCV000890262 | pathogenic | not provided | 2023-06-05 | criteria provided, single submitter | clinical testing | Nonsense variant predicted to result in protein truncation, as the last 54 amino acids are lost, and other loss-of-function variants have been reported downstream in HGMD; Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 17704778, 22957832, 19377476, 25525159, 26012578, 34356170, 33004838) |
OMIM | RCV000012153 | SCV000032387 | pathogenic | Syndromic X-linked intellectual disability 14 | 2013-06-01 | no assertion criteria provided | literature only |