Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002122169 | SCV002398704 | likely benign | not provided | 2023-12-03 | criteria provided, single submitter | clinical testing | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV004770406 | SCV005380642 | uncertain significance | not specified | 2024-08-12 | criteria provided, single submitter | clinical testing | Variant summary: COL11A2 c.2492C>T (p.Ser831Leu) results in a non-conservative amino acid change in the encoded protein sequence. Four of five in-silico tools predict a benign effect of the variant on protein function. The variant allele was found at a frequency of 7.2e-05 in 249930 control chromosomes. This frequency is not significantly higher than estimated for a pathogenic variant in COL11A2 causing COL11A2-Related Disorders, allowing no conclusion about variant significance. c.2492C>T has been reported in the literature in an individual affected with COL11A2-Related Disorders (Nishio_2015). These report(s) do not provide unequivocal conclusions about association of the variant with COL11A2-Related Disorders. To our knowledge, no experimental evidence demonstrating an impact on protein function has been reported. The following publication have been ascertained in the context of this evaluation (PMID: 25788563). ClinVar contains an entry for this variant (Variation ID: 1592134). Based on the evidence outlined above, the variant was classified as uncertain significance. |