Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000013084 | SCV003514080 | pathogenic | Hyper-IgM syndrome type 5 | 2022-10-27 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Pro131Hisfs*13) in the UNG gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in UNG are known to be pathogenic (PMID: 12958596). For these reasons, this variant has been classified as Pathogenic. ClinVar contains an entry for this variant (Variation ID: 12290). This variant is also known as 462C del. This premature translational stop signal has been observed in individual(s) with hyper IgM syndrome. (PMID: 12958596). This variant is present in population databases (rs778896112, gnomAD 0.005%). |
OMIM | RCV000013084 | SCV000033330 | pathogenic | Hyper-IgM syndrome type 5 | 2003-10-01 | no assertion criteria provided | literature only |