Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Baylor Genetics | RCV001329608 | SCV001521097 | uncertain significance | Hyper-IgM syndrome type 5 | 2019-06-30 | criteria provided, single submitter | clinical testing | This variant was determined to be of uncertain significance according to ACMG Guidelines, 2015 [PMID:25741868]. |
Labcorp Genetics |
RCV001329608 | SCV002130212 | uncertain significance | Hyper-IgM syndrome type 5 | 2021-06-24 | criteria provided, single submitter | clinical testing | This sequence change replaces glycine with arginine at codon 164 of the UNG protein (p.Gly164Arg). The glycine residue is highly conserved and there is a moderate physicochemical difference between glycine and arginine. This variant is present in population databases (rs745760429, ExAC 0.009%). This variant has not been reported in the literature in individuals with UNG-related conditions. ClinVar contains an entry for this variant (Variation ID: 1028541). Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Probably Damaging"; Align-GVGD: "Class C15"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |