Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002753597 | SCV003753945 | uncertain significance | Inborn genetic diseases | 2022-12-19 | criteria provided, single submitter | clinical testing | The c.2753C>T (p.A918V) alteration is located in exon 26 (coding exon 26) of the LRPPRC gene. This alteration results from a C to T substitution at nucleotide position 2753, causing the alanine (A) at amino acid position 918 to be replaced by a valine (V). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Revvity Omics, |
RCV003135273 | SCV003812765 | uncertain significance | Congenital lactic acidosis, Saguenay-Lac-Saint-Jean type | 2019-08-02 | criteria provided, single submitter | clinical testing |