Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV000152463 | SCV000201570 | uncertain significance | not specified | 2013-09-18 | criteria provided, single submitter | clinical testing | The Val3689Glufs variant in TTN has not been previously reported in individuals with cardiomyopathy or in large population studies. This frameshift variant is p redicted to alter the protein?s amino acid sequence beginning at position 3689 a nd lead to a premature termination codon 12 amino acids downstream. This alterat ion is then predicted to lead to a truncated or absent protein. Frameshift and o ther truncating variants in TTN are strongly associated with DCM (Herman 2012); however, this variant is located in an exon that is only present in a transcript (Novex-3) whose function is unclear. Additional information is needed to fully assess the clinical significance of this variant. |