Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV000146646 | SCV000193955 | likely pathogenic | Cornelia de Lange syndrome 1 | 2013-02-08 | criteria provided, single submitter | clinical testing | |
Gene |
RCV004815206 | SCV005439726 | likely pathogenic | not provided | 2024-06-19 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 38284454) |
Division of Human Genetics, |
RCV000146646 | SCV002552105 | likely pathogenic | Cornelia de Lange syndrome 1 | no assertion criteria provided | research |