Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
ARUP Laboratories, |
RCV002227330 | SCV002506175 | uncertain significance | Anemia, congenital dyserythropoietic, type 1a | 2022-01-26 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV003093895 | SCV002957026 | uncertain significance | not provided | 2023-08-14 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be tolerated. ClinVar contains an entry for this variant (Variation ID: 1679451). This variant has not been reported in the literature in individuals affected with CDAN1-related conditions. This variant is present in population databases (no rsID available, gnomAD 0.006%). This sequence change replaces serine, which is neutral and polar, with asparagine, which is neutral and polar, at codon 93 of the CDAN1 protein (p.Ser93Asn). |
St. |
RCV002227330 | SCV005402422 | uncertain significance | Anemia, congenital dyserythropoietic, type 1a | 2024-05-27 | criteria provided, single submitter | clinical testing | The CDAN1 c.278_279delinsAT (p.Ser93Asn) is an in-frame deletion-insertion. The variant is observed in gnomAD; however, the minor allele frequency cannot be estimated with certainty (https://gnomad.broadinstitute.org/). In silico evaluation of the impact of this variant on protein function cannot be determined, and functional studies have not been performed. This variant has not been reported in individuals with CDAN1-related congenital dyserythropoietic anemia. In summary, the evidence currently available is insufficient to determine the clinical significance of this variant. It has therefore been classified as of uncertain significance. |