Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV004723669 | SCV005329274 | uncertain significance | Immunodeficiency 98 with autoinflammation, X-linked | 2023-05-20 | criteria provided, single submitter | clinical testing | The observed missense c.328C>G(p.Gln110Glu) variant in TLR8 gene has not been reported previously as a pathogenic variant nor a benign variant, to our knowledge. The p.Gln110Glu variant is absent in gnomAD Exomes. This variant has not been submitted to the ClinVar database. Multiple lines of computational evidences (Polyphen - Benign, SIFT - Tolerated and MutationTaster - Polymorphism) predict no damaging effect on protein structure and function for this variant. The amino acid Gln at position 110 is changed to a Glu changing protein sequence and it might alter its composition and physico-chemical properties. For these reasons, this variant has been classified as a Variant of Uncertain Significance (VUS). |