Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Division of Genetic & Genomic Pathology, |
RCV004723632 | SCV005326510 | likely pathogenic | PPARG-related familial partial lipodystrophy; Type 2 diabetes mellitus | 2024-09-16 | criteria provided, single submitter | clinical testing | PPARG c.436dup is a frameshift variant, with a premature stop codon, and loss-of-function in the PPARG gene is a known mechanism of disease. This variant was not previously reported in population databases (gnomAD v2.1.1 and v4.1.0) and clinical databases (ClinVar, HGMD). |