Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001337284 | SCV001530880 | uncertain significance | Hyper-IgE recurrent infection syndrome 1, autosomal dominant; STAT3 gain of function | 2022-08-09 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Experimental studies and prediction algorithms are not available or were not evaluated, and the functional significance of this variant is currently unknown. This variant has been observed in individuals with hyper-IgE syndrome (PMID: 17881745, 23584561). This variant is not present in population databases (gnomAD no frequency). This variant, c.1931_1933del, results in the deletion of 1 amino acid(s) of the STAT3 protein (p.Gln644del), but otherwise preserves the integrity of the reading frame. |