Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV004785814 | SCV005400868 | likely pathogenic | Bardet-Biedl syndrome 8 | criteria provided, single submitter | clinical testing | The splice donor c.489+1G>A variant in the TTC8 gene has been reported previously in an individual affected with Bardet-Biedl Syndrome (Suspitsin et al., 2016). This variant is absent in the gnomAD Exomes. However study on multiple affected individuals and functional studies on the pathogenicity of the variant is unavailable. This variant change affects the donor splice site in intron 5 of the TTC8 gene. Loss of function variants have been previously reported to be disease causing (M'hamdi et al., 2014). For these reasons, this variant has been classified as Likely Pathogenic. |