Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clinical Genetics Laboratory, |
RCV004720217 | SCV005326490 | likely pathogenic | Bardet-Biedl syndrome | 2024-01-23 | criteria provided, single submitter | clinical testing | The SCLT1 variant c.1439+1del was present in the homozygous state in 1 patient. The patient's heterozygous sibling is unaffected. Consanguineous parents. The following ACMG criteria were applied in classifying this variant: PVS1, PM2 |