Total submissions: 1
| Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
|---|---|---|---|---|---|---|---|---|
| Laboratory for Molecular Medicine, |
RCV000151585 | SCV000199737 | pathogenic | Rare genetic deafness | 2014-09-09 | criteria provided, single submitter | clinical testing | The c.1688+1G>T variant in OTOA has not been previously reported in individuals with hearing loss or in large population studies. This variant occurs in the inv ariant region (+ 1/2) of the 5' splice consensus sequence and is predicted to ca use altered splicing leading to an abnormal or absent protein. In summary, this variant meets our criteria to be classified as pathogenic for hearing loss in an autosomal recessive manner. |