Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetics and Molecular Pathology, |
RCV003447665 | SCV004175212 | likely pathogenic | Familial cold autoinflammatory syndrome 2 | 2023-03-02 | criteria provided, single submitter | clinical testing | The NLRP12 c.2056_2057dup variant is classified as Likely Pathogenic (PVS1, PM2) This NLRP12 c.2056_2057dup variant is located in exon 3/10 and is predicted to cause a shift in the reading frame at codon 687 and the introduction of a premature termination codon 30 amino acids downstream (PVS1). This variant is absent from population databases (PM2). This variant has not been reported in dbSNP, ClinVar, HGMD or the scientific literature to date. |