Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000698166 | SCV000826810 | uncertain significance | Familial cold autoinflammatory syndrome 2 | 2018-04-27 | criteria provided, single submitter | clinical testing | This variant is present in population databases (rs143182167, ExAC 0.02%). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Probably Damaging"; Align-GVGD: "Class C0"). This variant has not been reported in the literature in individuals with NLRP12-related disease. This sequence change replaces phenylalanine with leucine at codon 28 of the NLRP12 protein (p.Phe28Leu). The phenylalanine residue is highly conserved and there is a small physicochemical difference between phenylalanine and leucine. |