Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Breda Genetics srl | RCV002293382 | SCV002586270 | likely pathogenic | Familial cold autoinflammatory syndrome 2 | 2022-08-17 | criteria provided, single submitter | clinical testing | The variant c.957del (p.Thr320Argfs*8) in the NLRP12 gene creates a shift in the reading frame which is predicted to result in a premature stop codon 8 amino acids downstream, which is likely to result in a truncated protein or protein loss due to nonsense-mediated messenger decay (NMD). There is no information on frequency in gnomAD or 1000 Genomes Project. Another frameshift variant c.958_959insGCTTAATT (p.Thr320fs), which falls one nucleotide downstream the variant c.957del (p.Thr320Argfs*8), is reported as likely pathogenic in ClinVar (Variation ID: 1324811). |