Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV000221773 | SCV000272576 | uncertain significance | not specified | 2017-07-11 | criteria provided, single submitter | clinical testing | The c.791-14G>C variant in TSPEAR has been previously reported by our laboratory in 1 individual with hearing loss, but a variant affecting the other copy of th e gene was not identified. This variant has been identified in 83/126028 Europea n chromosomes by the Genome Aggregation Database (gnomAD, http://gnomad.broadins titute.org; dbSNP rs199699551); however, this frequency is not high enough to ru le out a pathogenic role. This variant is located in the 3' splice region. Compu tational tools do not suggest an impact to splicing. However, this information i s not predictive enough to rule out pathogenicity. In summary, the clinical sig nificance of the c.791-14G>C variant is uncertain. |
Labcorp Genetics |
RCV002057180 | SCV002453448 | likely benign | not provided | 2024-10-22 | criteria provided, single submitter | clinical testing |